A Pediatric Case with the Diagnosis of Stevens Johnson Syndrome

Abstract

Stevens-Johnson syndrome (SJS) is a rare but life-threatening, mucocutaneous, T cell mediated hypersensitivity reaction. Most of the cases are triggered by a drug. Infections, vaccines, chemicals, systemic or malign diseases may have also roles in etiology. Disease generally starts with prodromal symptoms including fever, malaise, headache, myalgia or upper respiratory tract infection. There is no specific treatment modality for SJS.

Diagnosing the disease rapidly, discontinuation of the suspected drug immediately, and supportive therapy are the main steps in treatment. Medications like systemic steroids, intravenous immunglobulin (IVIG) and cyclosporin are also used in treatment.

Our aim in presenting a case of SJS is to increase awareness of this disease, to emphasize importance of immediate diagnosis and supportive therapy.